Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000494484 | SCV000582482 | pathogenic | not provided | 2015-09-03 | criteria provided, single submitter | clinical testing | The c.49dupC duplication in the FLCN gene causes a frameshift starting with codon Arginine 17, changes this amino acid to a Proline residue and creates a premature Stop codon at position 20 of the new reading frame, denoted p.Arg17ProfsX20. This variant is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. Therefore, we interpret c.49dupC as a pathogenic variant. |
Mendelics | RCV000989762 | SCV001140315 | pathogenic | Birt-Hogg-Dube syndrome | 2019-05-28 | criteria provided, single submitter | clinical testing | |
Centre for Mendelian Genomics, |
RCV001197006 | SCV001367641 | pathogenic | Potocki-Lupski syndrome | 2018-10-31 | criteria provided, single submitter | clinical testing | This variant was classified as: Pathogenic. The following ACMG criteria were applied in classifying this variant: PVS1,PS2,PM2. |
Juno Genomics, |
RCV004796200 | SCV005416722 | pathogenic | Birt-Hogg-Dube syndrome 1 | criteria provided, single submitter | clinical testing | PM2_Supporting+PVS1+PS2_Moderate |