Total submissions: 2
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Labcorp Genetics |
RCV000816840 | SCV000957366 | pathogenic | Birt-Hogg-Dube syndrome | 2018-12-04 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Phe188Serfs*35) in the FLCN gene. It is expected to result in an absent or disrupted protein product. This variant has been observed in a family with clinical features of Birt-Hogg-Dubé (BHD) syndrome (PMID: 26342594). Loss-of-function variants in FLCN are known to be pathogenic (PMID: 15852235). For these reasons, this variant has been classified as Pathogenic. |
| Ce |
RCV002292585 | SCV002585625 | pathogenic | not provided | 2022-08-01 | criteria provided, single submitter | clinical testing | FLCN: PVS1, PM2 |