Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Diagnostics Services |
RCV001527388 | SCV001738380 | likely pathogenic | Cardiospondylocarpofacial syndrome; Frontometaphyseal dysplasia 2 | 2021-01-25 | criteria provided, single submitter | clinical testing | The c.815C>A variant is not present in publicly available population databases like 1000 Genomes, Exome Variant Server (EVS), Exome Aggregation Consortium (ExAC), Genome Aggregation Database (gnomAD) and dbSNP. The variant is not present in our in-house exome database.The variant was not reported earlier to ClinVar, Human Genome Mutation Database (HGMD) and OMIM datanbases. In-silico pathogenicity prediction programs like SIFT, Polyphen-2, MutationTaster2, CADD, InterVar, Varsome etc. predicted this variant to be likely deleterious. However there are no reported or established functional studies present to prove it's pathogenicity. Due to lack of enough evidence the variant has been classified as Likely Pathogenic. |