Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Biological Sciences, |
RCV001195079 | SCV001250886 | pathogenic | Intellectual disability | 2016-05-12 | no assertion criteria provided | clinical testing | Component of the DNA damage/stress response pathway that functions downstream of p53/TP53 and can either promote cell survival or apoptosis. Associated with CRADD and the CASP2 caspase, it forms the PIDDosome a complex that activates CASP2 and triggers apoptosis. |
OMIM | RCV002249778 | SCV002520441 | pathogenic | Intellectual developmental disorder, autosomal recessive 75, with neuropsychiatric features and variant lissencephaly | 2022-04-20 | no assertion criteria provided | literature only |