Total submissions: 1
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Clinical Genomics Laboratory, |
RCV004555950 | SCV005045028 | uncertain significance | Intellectual developmental disorder, autosomal recessive 75, with neuropsychiatric features and variant lissencephaly | 2023-11-21 | criteria provided, single submitter | clinical testing | The PIDD1 c.76G>A (p.Gly26Arg) variant, to our knowledge, has not been reported in the medical literature. This variant is only observed on 3 out of 278,172 alleles in the general population (gnomAD v.2.1.1), indicating it is not a common variant. Computational predictors suggest that the variant does not impact PIDD1 function. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |