Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000672151 | SCV000797222 | likely pathogenic | Ellis-van Creveld syndrome | 2018-01-17 | criteria provided, single submitter | clinical testing | |
Kasturba Medical College, |
RCV001290312 | SCV001478359 | likely pathogenic | Curry-Hall syndrome | 2019-05-12 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003767995 | SCV004607358 | pathogenic | Ellis-van Creveld syndrome; Curry-Hall syndrome | 2023-07-29 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 556185). This variant has not been reported in the literature in individuals affected with EVC2-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Leu18Serfs*38) in the EVC2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in EVC2 are known to be pathogenic (PMID: 17024374, 19810119, 19876929). |