Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001753398 | SCV001986365 | uncertain significance | not provided | 2019-08-26 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; This variant is associated with the following publications: (PMID: 12145746, 16389551, 24949729, 30303587, 26186295) |
OMIM | RCV000003557 | SCV000023715 | pathogenic | Autosomal recessive nonsyndromic hearing loss 6 | 2002-09-01 | no assertion criteria provided | literature only | |
University of Washington Center for Mendelian Genomics, |
RCV001291482 | SCV001479986 | likely pathogenic | Hearing loss, autosomal recessive | no assertion criteria provided | research |