Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001361322 | SCV001557295 | uncertain significance | not provided | 2022-05-10 | criteria provided, single submitter | clinical testing | This sequence change replaces isoleucine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 77 of the CLDN19 protein (p.Ile77Val). This variant is present in population databases (rs140190002, gnomAD 0.2%). This variant has not been reported in the literature in individuals affected with CLDN19-related conditions. ClinVar contains an entry for this variant (Variation ID: 1053033). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C25"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002488098 | SCV002776806 | likely benign | Renal hypomagnesemia 5 with ocular involvement | 2024-03-14 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002547770 | SCV003752342 | uncertain significance | Inborn genetic diseases | 2021-10-20 | criteria provided, single submitter | clinical testing | The c.229A>G (p.I77V) alteration is located in exon 2 (coding exon 2) of the CLDN19 gene. This alteration results from a A to G substitution at nucleotide position 229, causing the isoleucine (I) at amino acid position 77 to be replaced by a valine (V). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Prevention |
RCV003898343 | SCV004709313 | likely benign | CLDN19-related disorder | 2024-02-01 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |