Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000689419 | SCV000817067 | uncertain significance | Congenital myopathy 4B, autosomal recessive; Congenital myopathy with fiber type disproportion | 2022-08-06 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Variants that disrupt the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). Studies have shown that this variant is associated with altered splicing resulting in multiple RNA products (PMID: 12196661). ClinVar contains an entry for this variant (Variation ID: 12448). This variant has been observed in individual(s) with autosomal recessive congenital myopathy (PMID: 12196661). This variant is present in population databases (rs113605263, gnomAD 0.01%). This sequence change falls in intron 9 of the TPM3 gene. It does not directly change the encoded amino acid sequence of the TPM3 protein. It affects a nucleotide within the consensus splice site. |
Revvity Omics, |
RCV000128706 | SCV003820937 | uncertain significance | not provided | 2022-03-25 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000013261 | SCV000033508 | pathogenic | Congenital myopathy 4B, autosomal recessive | 2002-08-27 | no assertion criteria provided | literature only | |
TPM3 homepage - |
RCV000128706 | SCV000172346 | not provided | not provided | no assertion provided | not provided |