Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003144993 | SCV003830679 | uncertain significance | Filippi syndrome | 2019-02-13 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV003144993 | SCV004047757 | uncertain significance | Filippi syndrome | criteria provided, single submitter | clinical testing | The missense variant c.1283A>G (p.Gln428Arg) in CKAP2L gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Gln428Arg variant is reported as 0.01% in gnomAD exomes and not present in 1000 Genome database. The amino acid Gln at position 428 is changed to a Arg changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Uncertain Significance . | |
Ambry Genetics | RCV004246120 | SCV004928849 | uncertain significance | Inborn genetic diseases | 2023-10-17 | criteria provided, single submitter | clinical testing | The c.1283A>G (p.Q428R) alteration is located in exon 4 (coding exon 4) of the CKAP2L gene. This alteration results from a A to G substitution at nucleotide position 1283, causing the glutamine (Q) at amino acid position 428 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |