Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV000513131 | SCV000609317 | uncertain significance | not provided | 2017-02-01 | criteria provided, single submitter | clinical testing | |
Genetic Services Laboratory, |
RCV001821432 | SCV002067626 | uncertain significance | not specified | 2018-11-16 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002524972 | SCV003450119 | uncertain significance | Cohen syndrome | 2022-05-10 | criteria provided, single submitter | clinical testing | This sequence change replaces proline, which is neutral and non-polar, with histidine, which is basic and polar, at codon 1221 of the VPS13B protein (p.Pro1221His). This variant is present in population databases (rs757707584, gnomAD 0.002%). This variant has not been reported in the literature in individuals affected with VPS13B-related conditions. ClinVar contains an entry for this variant (Variation ID: 444761). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Not Available"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |