Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000667304 | SCV000791735 | uncertain significance | Bardet-Biedl syndrome 12 | 2017-05-23 | criteria provided, single submitter | clinical testing | |
Invitae | RCV001855478 | SCV002212499 | uncertain significance | Bardet-Biedl syndrome | 2021-08-28 | criteria provided, single submitter | clinical testing | This variant, c.1681_1683del, results in the deletion of 1 amino acid(s) of the BBS12 protein (p.Glu561del), but otherwise preserves the integrity of the reading frame. This variant is not present in population databases (ExAC no frequency). This variant has not been reported in the literature in individuals affected with BBS12-related conditions. ClinVar contains an entry for this variant (Variation ID: 552099). Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |