Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV002227762 | SCV002506867 | uncertain significance | Monosomy 7 myelodysplasia and leukemia syndrome 1; Ataxia-pancytopenia syndrome | 2021-07-02 | criteria provided, single submitter | clinical testing | The heterozygous c.2052A>C (p.Glu684Asp) missense variant identified in the SAMD9L gene has not been reported in affected individuals in the literature. The variant is absent from gnomAD(v3) database suggesting it is not a common benign variant in the populations represented in that database. The variant affects a conserved residue and is predicted deleterious by multiple in silico prediction tools. Based on the available evidence, the heterozygous c.2052A>C(p.Glu684Asp) missense variant identified in the SAMD9L gene is reported as a variant of uncertain significance. |