Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
SIB Swiss Institute of Bioinformatics | RCV001815046 | SCV002540191 | uncertain significance | Congenital disorder of glycosylation, type Iw, autosomal dominant | 2022-06-16 | criteria provided, single submitter | curation | This variant is interpreted as variant of uncertain significance for congenital disorder of glycosylation 1W, autosomal dominant. The following ACMG Tag(s) were applied: Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium (PM2); Multiple lines of computational evidence support a deleterious effect on the gene or gene product (PP3); Well-established functional studies show a deleterious effect (PS3 downgraded to moderate). |
OMIM | RCV001815046 | SCV002061885 | pathogenic | Congenital disorder of glycosylation, type Iw, autosomal dominant | 2022-01-20 | no assertion criteria provided | literature only |