Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000348806 | SCV000340618 | uncertain significance | not provided | 2016-04-21 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001360586 | SCV001556511 | uncertain significance | Nephronophthisis | 2023-07-03 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt NPHP3 protein function. ClinVar contains an entry for this variant (Variation ID: 286995). This variant has not been reported in the literature in individuals affected with NPHP3-related conditions. This variant is present in population databases (rs759153335, gnomAD 0.02%). This sequence change replaces alanine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 1021 of the NPHP3 protein (p.Ala1021Val). |
Gene |
RCV000348806 | SCV001993496 | uncertain significance | not provided | 2019-08-21 | criteria provided, single submitter | clinical testing | In silico analysis, which includes protein predictors and evolutionary conservation, supports that this variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Fulgent Genetics, |
RCV002502141 | SCV002812770 | uncertain significance | Renal-hepatic-pancreatic dysplasia 1; Nephronophthisis 3; NPHP3-related Meckel-like syndrome | 2021-12-16 | criteria provided, single submitter | clinical testing |