Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003067998 | SCV003451628 | benign | not provided | 2024-11-20 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003155509 | SCV003844210 | uncertain significance | not specified | 2023-02-24 | criteria provided, single submitter | clinical testing | Variant summary: BRWD3 c.4384A>G (p.Ser1462Gly) results in a non-conservative amino acid change in the encoded protein sequence. Two of four in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 2.7e-05 in 183156 control chromosomes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.4384A>G in individuals affected with Intellectual Disability, X-Linked 93 and no experimental evidence demonstrating its impact on protein function have been reported. One clinical diagnostic laboratory has submitted clinical-significance assessments for this variant to ClinVar after 2014 without evidence for independent evaluation and classified the variant as uncertain significance. Based on the evidence outlined above, the variant was classified as uncertain significance. |
Illumina Laboratory Services, |
RCV003985112 | SCV004801451 | uncertain significance | Intellectual disability, X-linked 93 | 2020-04-14 | criteria provided, single submitter | clinical testing | The BRWD3 c.4384A>G p.(Ser1462Gly) missense variant is a missense variant. To our knowledge, this variant has not been reported in the peer-reviewed literature. The highest frequency of this allele in the Genome Aggregation Database is 0.000037 in the European (non-Finnish) population (version 2.1.1). Based on the limited evidence, the c.4384A>G p.(Ser1462Gly) variant is classified as a variant of uncertain significance for intellectual development disorder. |