Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV000261591 | SCV000475314 | uncertain significance | Nephronophthisis | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000300363 | SCV000475315 | uncertain significance | Meckel-Gruber syndrome | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000367005 | SCV000475316 | uncertain significance | Familial aplasia of the vermis | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002523704 | SCV003521536 | uncertain significance | Familial aplasia of the vermis; Meckel-Gruber syndrome | 2022-09-19 | criteria provided, single submitter | clinical testing | This variant, c.125_130dup, results in the insertion of 2 amino acid(s) of the TMEM67 protein (p.Pro42_Phe43dup), but otherwise preserves the integrity of the reading frame. This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with TMEM67-related conditions. ClinVar contains an entry for this variant (Variation ID: 363918). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |