Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Servicio de Genética Del Instituto Nacional de Salud Del Niño, |
RCV004794745 | SCV005414477 | uncertain significance | Kleefstra syndrome 2 | 2024-11-18 | criteria provided, single submitter | clinical testing | The variant NM_170606.3:c.1513G>A, p.Asp505Asn results in the substitution of aspartic acid with asparagine at position 505 in the protein. Aspartic acid is a negatively charged amino acid, while asparagine is neutral. This substitution may affect the protein's structure or function due to the loss of charge. Based on ACMG/AMP guidelines, PM2 (absent in population databases), the variant is classified as uncertain significance. |