Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Servicio de Genética Del Instituto Nacional de Salud Del Niño, |
RCV004794743 | SCV005414474 | uncertain significance | Kleefstra syndrome 2 | 2024-11-18 | criteria provided, single submitter | clinical testing | The variant NM_170606.3:c.6401C>A, p.Pro2134His results in the substitution of proline with histidine at position 2134 in the protein. Proline is a structurally rigid amino acid, and its substitution with histidine, which has a polar imidazole side chain, could affect the protein's structure and function. According to ACMG/AMP guidelines, based on evidence from PM2, this variant is classified as uncertain significance. |