Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001367857 | SCV001564225 | likely benign | Charcot-Marie-Tooth disease type 2 | 2024-05-06 | criteria provided, single submitter | clinical testing | |
Genetic Services Laboratory, |
RCV001820069 | SCV002068284 | likely benign | not specified | 2018-01-16 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV005401831 | SCV006062337 | uncertain significance | Cardiomyopathy | 2024-01-03 | criteria provided, single submitter | clinical testing | This variant causes a C to A nucleotide substitution at the -7 position of intron 5 of the LMNA gene. Splice site prediction tools are inconclusive regarding the impact of this variant on RNA splicing. To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with LMNA-related disorders in the literature. This variant has been identified in 1/246476 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |