Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001046691 | SCV001210605 | uncertain significance | Early infantile epileptic encephalopathy with suppression bursts | 2019-04-18 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has been reported to affect KCNQ2 protein function (PMID: 16597729). This variant has not been reported in the literature in individuals with KCNQ2-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change replaces leucine with proline at codon 585 of the KCNQ2 protein (p.Leu585Pro). The leucine residue is highly conserved and there is a moderate physicochemical difference between leucine and proline. |