Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003753044 | SCV004523222 | uncertain significance | Early infantile epileptic encephalopathy with suppression bursts | 2023-08-04 | criteria provided, single submitter | clinical testing | This sequence change affects codon 23 of the KCNQ2 mRNA. It is a 'silent' change, meaning that it does not change the encoded amino acid sequence of the KCNQ2 protein. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. This variant has not been reported in the literature in individuals affected with KCNQ2-related conditions. This variant is not present in population databases (gnomAD no frequency). |