Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002052243 | SCV002318836 | uncertain significance | Autosomal recessive congenital ichthyosis 4A | 2022-03-22 | criteria provided, single submitter | clinical testing | Same or different nucleotide change resulting in same amino acid change has been previously reported to be associated with ABCA12 related disorder (PMID:22257947). The variant is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: [0.0000040). In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.869>=0.6, 3CNET: 0.991>=0.75). Therefore, this variant is classified as uncertain significance according to the recommendation of ACMG/AMP guideline. |