Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000426277 | SCV000516687 | pathogenic | not provided | 2015-04-29 | criteria provided, single submitter | clinical testing | The R362X variant in the CYP4F22 gene has not been reported previously as a pathogenic variant and it was also not observed in approximately 6,500 individuals of European and African Americanancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in thesepopulations. This variant is predicted to cause loss of normal protein function either through proteintruncation or nonsense-mediated mRNA decay. Therefore, we interpret R362X as a pathogenic variant. |
Institute for Human Genetics, |
RCV000678436 | SCV000804510 | pathogenic | Autosomal recessive congenital ichthyosis 5 | 2018-04-23 | no assertion criteria provided | clinical testing |