Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003340685 | SCV004047326 | uncertain significance | Polycystic kidney disease 5 | criteria provided, single submitter | clinical testing | The splice region variant c.1000-4T>C in DZIP1L (NM_173543.3) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The c.1000-4T>C variant is observed in 7/30,598 (0.0229%) alleles from individuals of South Asian background in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. The c.1000-4T>C variant is not predicted to disrupt splicing by any splice site algorithm. The nucleotide c.1000-4T>C in DZIP1L is not conserved according to a GERP++ and PhyloP analysis of 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance |