Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Human Genetics, |
RCV001261513 | SCV001438312 | pathogenic | Intellectual disability, FRA12A type | 2020-10-19 | criteria provided, single submitter | research | The variant was found in heterozygosis in two siblings presenting learning disabilities, speech impairment, and microcephaly. |
Genetic Endocrinology Unit / Unidade de Endocrinologia Genetica - |
RCV001261513 | SCV005043063 | uncertain significance | Intellectual disability, FRA12A type | 2024-05-07 | criteria provided, single submitter | clinical testing | Rare variant (PM2) in a consensus splice site identified in a patient with no neurological phenotype. The variant is also present in her healthy father (BS2). The phenotype caused by heterozygosity of LoF-type variants is not established. In silico analysis predicts that the variant may alter splice processing (PP3). |