Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001246418 | SCV001419772 | uncertain significance | not provided | 2022-10-17 | criteria provided, single submitter | clinical testing | This sequence change replaces glycine, which is neutral and non-polar, with glutamic acid, which is acidic and polar, at codon 136 of the CLRN1 protein (p.Gly136Glu). This variant is present in population databases (rs779258184, gnomAD 0.2%). This missense change has been observed in individual(s) with clinical features of CLRN1-related conditions (PMID: 31960602). ClinVar contains an entry for this variant (Variation ID: 556027). Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Myriad Genetics, |
RCV001810476 | SCV002060315 | uncertain significance | Usher syndrome type 3A | 2021-10-01 | criteria provided, single submitter | clinical testing | NM_174878.2(CLRN1):c.407G>A(G136E) is a missense variant classified as a variant of uncertain significance in the context of Usher syndrome type 3. G136E has been observed in cases with relevant disease (PMID: 27610647, 28471114, 25268133, 31960602, 31213501). Functional assessments of this variant are not available in the literature. G136E has been observed in population frequency databases (gnomAD: EAS 0.17%). In summary, there is insufficient evidence to classify NM_174878.2(CLRN1):c.407G>A(G136E) as pathogenic or benign. Please note: this variant was assessed in the context of healthy population screening. |
Dept Of Ophthalmology, |
RCV003889961 | SCV004705690 | uncertain significance | Retinal dystrophy | 2023-10-01 | criteria provided, single submitter | research | |
Natera, |
RCV000671965 | SCV002081532 | uncertain significance | Usher syndrome type 3 | 2020-01-10 | no assertion criteria provided | clinical testing |