Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002419157 | SCV002678655 | uncertain significance | Maturity onset diabetes mellitus in young | 2019-02-08 | criteria provided, single submitter | clinical testing | The p.S3R variant (also known as c.7A>C), located in coding exon 1 of the HNF4A gene, results from an A to C substitution at nucleotide position 7. The serine at codon 3 is replaced by arginine, an amino acid with dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
New York Genome Center | RCV003228075 | SCV003925105 | uncertain significance | Maturity-onset diabetes of the young type 1; Type 2 diabetes mellitus; Fanconi renotubular syndrome 4 with maturity-onset diabetes of the young | 2022-02-23 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003730143 | SCV004525820 | likely benign | not provided | 2023-02-27 | criteria provided, single submitter | clinical testing |