Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000546568 | SCV000658160 | likely benign | DICER1-related tumor predisposition | 2025-01-08 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001013829 | SCV001174464 | uncertain significance | Hereditary cancer-predisposing syndrome | 2025-02-18 | criteria provided, single submitter | clinical testing | The p.K652T variant (also known as c.1955A>C), located in coding exon 11 of the DICER1 gene, results from an A to C substitution at nucleotide position 1955. The lysine at codon 652 is replaced by threonine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV003470772 | SCV004193311 | uncertain significance | Global developmental delay - lung cysts - overgrowth - Wilms tumor syndrome | 2023-11-27 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003409829 | SCV004113391 | uncertain significance | DICER1-related disorder | 2024-05-22 | no assertion criteria provided | clinical testing | The DICER1 c.1955A>C variant is predicted to result in the amino acid substitution p.Lys652Thr. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.029% of alleles in individuals of Latino descent in gnomAD. In ClinVar this variant has been interpreted ranging from likely benign to uncertain (https://ncbi.nlm.nih.gov/clinvar/variation/477076/). Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |