Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000227606 | SCV000291630 | uncertain significance | DICER1-related tumor predisposition | 2016-03-27 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 13 of the DICER1 mRNA. It does not directly change the encoded amino acid sequence of the DICER1 protein. This variant is not present in population databases (ExAC no frequency) and has not been reported in the literature in individuals with a DICER1-related disease. Algorithms developed to predict the effect of nucleotide changes on mRNA splicing suggest that this intronic variant may alter mRNA splicing, but this prediction has not been confirmed by published transcriptional studies. In summary, this is a novel intronic change with uncertain impact on splicing. It has been classified as a Variant of Uncertain Significance. |