Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
St. |
RCV005055252 | SCV005688992 | pathogenic | Pleuropulmonary blastoma | 2024-07-08 | criteria provided, single submitter | clinical testing | The DICER1 c.3579_3594dup (p.Gly1199GlnfsTer41) change duplicates sixteen nucleotides to cause a frameshift and the creation of a premature stop codon. This change is predicted to cause protein truncation or absence of protein due to nonsense-mediated decay. This variant has been reported in an individual whose tumor harbored a second pathogenic variant in the DICER1 gene (internal data). This variant is also absent in gnomAD v2.1.1 (https://gnomad.broadinstitute.org/). In summary, this variant meets criteria to be classified as pathogenic. |