Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000417892 | SCV000517986 | uncertain significance | not provided | 2019-08-05 | criteria provided, single submitter | clinical testing | In silico analysis, which includes protein predictors and evolutionary conservation, supports that this variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV000541177 | SCV000655323 | uncertain significance | Developmental and epileptic encephalopathy, 25 | 2022-08-09 | criteria provided, single submitter | clinical testing | This sequence change replaces valine, which is neutral and non-polar, with methionine, which is neutral and non-polar, at codon 458 of the SLC13A5 protein (p.Val458Met). This variant is present in population databases (rs372801738, gnomAD 0.03%). This variant has not been reported in the literature in individuals affected with SLC13A5-related conditions. ClinVar contains an entry for this variant (Variation ID: 380207). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The methionine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ce |
RCV000417892 | SCV001961649 | likely benign | not provided | 2022-09-01 | criteria provided, single submitter | clinical testing | SLC13A5: BP4, BP5 |
Genome- |
RCV000541177 | SCV002055640 | uncertain significance | Developmental and epileptic encephalopathy, 25 | 2021-07-15 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002379316 | SCV002697221 | uncertain significance | Inborn genetic diseases | 2022-10-12 | criteria provided, single submitter | clinical testing | The c.1372G>A (p.V458M) alteration is located in exon 10 (coding exon 10) of the SLC13A5 gene. This alteration results from a G to A substitution at nucleotide position 1372, causing the valine (V) at amino acid position 458 to be replaced by a methionine (M). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |