Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000807855 | SCV000947931 | pathogenic | Developmental and epileptic encephalopathy, 25 | 2018-12-21 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Trp103*) in the SLC13A5 gene. It is expected to result in an absent or disrupted protein product. For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in SLC13A5 are known to be pathogenic (PMID: 24995870, 26384929). This variant has not been reported in the literature in individuals with SLC13A5-related conditions. This variant is not present in population databases (ExAC no frequency). |