Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002228055 | SCV002508906 | pathogenic | not provided | 2024-08-16 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with tryptophan, which is neutral and slightly polar, at codon 177 of the C8orf37 protein (p.Arg177Trp). This variant is present in population databases (rs387907136, gnomAD 0.01%). This missense change has been observed in individuals with cone-rod dystrophy (PMID: 22177090, 25515582, 30029497, 31456290). It has also been observed to segregate with disease in related individuals. ClinVar contains an entry for this variant (Variation ID: 31194). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. Experimental studies have shown that this missense change affects C8orf37 function (PMID: 27008867). For these reasons, this variant has been classified as Pathogenic. |
Ophthalmic Genetics Group, |
RCV004794345 | SCV005415454 | likely pathogenic | Retinal dystrophy | 2024-05-27 | criteria provided, single submitter | research | |
OMIM | RCV000024193 | SCV000045484 | pathogenic | Cone-rod dystrophy 16 | 2012-01-13 | no assertion criteria provided | literature only | |
OMIM | RCV000477682 | SCV000564238 | pathogenic | Bardet-biedl syndrome 21 | 2012-01-13 | no assertion criteria provided | literature only | |
Sharon lab, |
RCV001002908 | SCV001160943 | likely pathogenic | Retinitis pigmentosa | 2019-06-23 | no assertion criteria provided | research | |
Faculty of Health Sciences, |
RCV001257837 | SCV001434700 | pathogenic | Autosomal recessive retinitis pigmentosa | 2015-09-10 | no assertion criteria provided | literature only |