Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute for Human Genetics, |
RCV000490814 | SCV000576469 | pathogenic | Autosomal recessive congenital ichthyosis 2 | 2016-07-01 | criteria provided, single submitter | clinical testing | In a 3-year-old Turkish girl with autosomal recessive congenital ichthyosis manifesting as congenital ichthyosiform erythroderma (ARCI2; 242100), we identified compound heterozygosity for the insertion p.Met122Asnfs*73 and the missense mutation p.Arg274Gln. |
OMIM | RCV000495827 | SCV000583584 | pathogenic | Ichthyosis, congenital, autosomal recessive 14 | 2017-07-13 | no assertion criteria provided | literature only |