Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Lupski Lab, |
RCV000224057 | SCV000292319 | pathogenic | Cataract 46 juvenile-onset | 2015-11-01 | criteria provided, single submitter | research | This variant co-segregates with juvenile cataracts in 39 family members (including 17 affected individuals [homozygous], 22 obligate carriers) across multiple sibships within a large Hutterite population. A potential association with sudden cardiac death is also observed. |
OMIM | RCV000224057 | SCV000280597 | pathogenic | Cataract 46 juvenile-onset | 2020-02-13 | no assertion criteria provided | literature only |