Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002006634 | SCV002296820 | uncertain significance | Emery-Dreifuss muscular dystrophy 5, autosomal dominant | 2022-11-16 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 1506307). This variant has not been reported in the literature in individuals affected with SYNE2-related conditions. This variant is present in population databases (rs140863307, gnomAD 0.07%), and has an allele count higher than expected for a pathogenic variant. This sequence change replaces alanine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 5240 of the SYNE2 protein (p.Ala5240Val). |
Fulgent Genetics, |
RCV002006634 | SCV005629403 | uncertain significance | Emery-Dreifuss muscular dystrophy 5, autosomal dominant | 2024-05-24 | criteria provided, single submitter | clinical testing |