Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Breda Genetics srl | RCV002293384 | SCV002586275 | likely pathogenic | Emery-Dreifuss muscular dystrophy 4, autosomal dominant | 2022-07-15 | criteria provided, single submitter | clinical testing | The variant c.18382-1G>A in the SYNE1 gene affects the acceptor splice site of intron 97 and is therefore highly likely to impact the splicing process by causing the exclusion of the following exons from the mature transcript and the translation of an aberrant protein or a shift in the reading frame. The variant is reported with an estimated allele frequency of 0.000003989 in gnomAD exomes with no homozygous individuals reported. |