Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000647632 | SCV000769430 | uncertain significance | Autosomal recessive ataxia, Beauce type; Emery-Dreifuss muscular dystrophy 4, autosomal dominant | 2024-03-28 | criteria provided, single submitter | clinical testing | This sequence change replaces histidine, which is basic and polar, with arginine, which is basic and polar, at codon 8360 of the SYNE1 protein (p.His8360Arg). This variant is present in population databases (rs375476506, gnomAD 0.05%). This variant has not been reported in the literature in individuals affected with SYNE1-related conditions. ClinVar contains an entry for this variant (Variation ID: 538392). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Athena Diagnostics | RCV000713648 | SCV000844275 | benign | not provided | 2018-04-19 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV000713648 | SCV003824732 | uncertain significance | not provided | 2020-10-25 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV005046832 | SCV005665951 | uncertain significance | Autosomal recessive ataxia, Beauce type; Emery-Dreifuss muscular dystrophy 4, autosomal dominant; Arthrogryposis multiplex congenita 3, myogenic type | 2024-05-01 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV005046832 | SCV006054675 | uncertain significance | Autosomal recessive ataxia, Beauce type; Emery-Dreifuss muscular dystrophy 4, autosomal dominant; Arthrogryposis multiplex congenita 3, myogenic type | 2021-12-03 | criteria provided, single submitter | research | |
Prevention |
RCV004544876 | SCV004786852 | uncertain significance | SYNE1-related disorder | 2024-02-19 | no assertion criteria provided | clinical testing | The SYNE1 c.25079A>G variant is predicted to result in the amino acid substitution p.His8360Arg. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.035% of alleles in individuals of East Asian descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |