Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004561376 | SCV005049023 | uncertain significance | Dyskeratosis congenita | 2024-02-13 | criteria provided, single submitter | clinical testing | The p.Q34P variant (also known as c.101A>C), located in coding exon 1 of the TERT gene, results from an A to C substitution at nucleotide position 101. The glutamine at codon 34 is replaced by proline, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |