Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute for Clinical Genetics, |
RCV003237583 | SCV002010759 | uncertain significance | not provided | 2021-11-03 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004558644 | SCV005049098 | uncertain significance | Dyskeratosis congenita | 2023-06-16 | criteria provided, single submitter | clinical testing | The p.T363I variant (also known as c.1088C>T), located in coding exon 2 of the TERT gene, results from a C to T substitution at nucleotide position 1088. The threonine at codon 363 is replaced by isoleucine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |