Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Department of Medical Genomics, |
RCV004801955 | SCV005420272 | likely pathogenic | Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1 | 2024-12-04 | criteria provided, single submitter | clinical testing | This variant is detected in a patient with pulmonary fibrosis with a strong family history. There is also evidence of myelodysplastic syndrome. This 16bp duplication leads to a premature termination codon, p.(Pro404Glnfs*140) and the transcript is expected to be subject to nonsense mediated decay. This variant has been observed at a very low frequency in control population database (variant allelic frequency 0.0002%, gnomAD v4.1.0). |