Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000502511 | SCV000597468 | uncertain significance | not specified | 2016-11-30 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002524311 | SCV001495495 | likely benign | Dyskeratosis congenita, autosomal dominant 2; Idiopathic Pulmonary Fibrosis | 2023-02-16 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004822081 | SCV005512346 | uncertain significance | Dyskeratosis congenita | 2024-08-27 | criteria provided, single submitter | clinical testing | The p.L488F variant (also known as c.1462C>T), located in coding exon 2 of the TERT gene, results from a C to T substitution at nucleotide position 1462. The leucine at codon 488 is replaced by phenylalanine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |