Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002555892 | SCV001235235 | likely benign | Dyskeratosis congenita, autosomal dominant 2; Idiopathic Pulmonary Fibrosis | 2023-11-27 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004559900 | SCV005049061 | uncertain significance | Dyskeratosis congenita | 2024-02-02 | criteria provided, single submitter | clinical testing | The p.G527V variant (also known as c.1580G>T), located in coding exon 3 of the TERT gene, results from a G to T substitution at nucleotide position 1580. The glycine at codon 527 is replaced by valine, an amino acid with dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |