Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004560110 | SCV003869002 | uncertain significance | Dyskeratosis congenita | 2022-11-16 | criteria provided, single submitter | clinical testing | The p.A532V variant (also known as c.1595C>T), located in coding exon 3 of the TERT gene, results from a C to T substitution at nucleotide position 1595. The alanine at codon 532 is replaced by valine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |