Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002539066 | SCV001011601 | likely benign | Dyskeratosis congenita, autosomal dominant 2; Idiopathic Pulmonary Fibrosis | 2023-12-30 | criteria provided, single submitter | clinical testing | |
Genetic Services Laboratory, |
RCV001816992 | SCV002064948 | likely benign | not specified | 2017-08-28 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004559730 | SCV002736993 | likely benign | Dyskeratosis congenita | 2022-02-26 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Prevention |
RCV004538290 | SCV004713842 | likely benign | TERT-related disorder | 2022-02-21 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |