Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002530150 | SCV000650757 | likely benign | Dyskeratosis congenita, autosomal dominant 2; Idiopathic Pulmonary Fibrosis | 2024-12-02 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV001788284 | SCV002030239 | uncertain significance | Dyskeratosis congenita, autosomal dominant 2 | 2021-02-09 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Baylor Genetics | RCV001788284 | SCV005052968 | uncertain significance | Dyskeratosis congenita, autosomal dominant 2 | 2024-02-28 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV005034104 | SCV005672280 | uncertain significance | Acute myeloid leukemia; Dyskeratosis congenita, autosomal dominant 2; Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1; Melanoma, cutaneous malignant, susceptibility to, 9 | 2024-06-20 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004543199 | SCV004773660 | uncertain significance | TERT-related disorder | 2024-01-12 | no assertion criteria provided | clinical testing | The TERT c.2744G>A variant is predicted to result in the amino acid substitution p.Gly915Asp. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.026% of alleles in individuals of Latino descent in gnomAD. It is interpreted as uncertain significance in ClinVar (https://preview.ncbi.nlm.nih.gov/clinvar/variation/471875/). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |