Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002548055 | SCV002123980 | likely benign | Dyskeratosis congenita, autosomal dominant 2; Idiopathic Pulmonary Fibrosis | 2023-09-15 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004558679 | SCV002748957 | uncertain significance | Dyskeratosis congenita | 2018-10-24 | criteria provided, single submitter | clinical testing | The p.G916S variant (also known as c.2746G>A), located in coding exon 11 of the TERT gene, results from a G to A substitution at nucleotide position 2746. The glycine at codon 916 is replaced by serine, an amino acid with similar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |