Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004821824 | SCV005512422 | uncertain significance | Dyskeratosis congenita | 2024-08-19 | criteria provided, single submitter | clinical testing | The p.V160A variant (also known as c.479T>C), located in coding exon 2 of the TERT gene, results from a T to C substitution at nucleotide position 479. The valine at codon 160 is replaced by alanine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |