Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001552739 | SCV001773484 | uncertain significance | not provided | 2021-05-11 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports that this variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 30523342, 29463756) |
Ambry Genetics | RCV004822415 | SCV005512323 | uncertain significance | Dyskeratosis congenita | 2024-08-07 | criteria provided, single submitter | clinical testing | The p.V170L variant (also known as c.508G>C), located in coding exon 2 of the TERT gene, results from a G to C substitution at nucleotide position 508. The valine at codon 170 is replaced by leucine, an amino acid with highly similar properties. This variant was reported in an individual with features consistent with a telomeropathy(Gutierrez-Rodrigues F et al. Genet Med, 2019 Jul;21:1594-1602). This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |